Embryonal Rhabdomyosarcoma - A Mimicker of Squamosal Otitis Media

Iranian Journal of Otorhinolaryngology

Ajay Bhandarkar¹  Kailesh Pujary¹  Architha Menon¹  Ranjini Kudva² 

[1] Department of Otorhinolaryngology, Kasturba Medical College, Manipal Academy of Higher Education Madhavnagar Manipal - 576104.;Department of Pathology, Kasturba Medical College, Manipal Academy of Higher Education Manipal.;

关键词: rhabdomyosarcoma;    chemotherapy;    radiotherapy;    acute facial paralysis;    pediatric;    temporal bone;   

DOI  :  10.22038/ijorl.2019.38807.2280

来源: DOAJ

【 摘 要 】

Introduction: Rhabdomyosarcoma is the most frequently occurring intrusive soft tissue sarcoma in the pediatric age group. Orbit is the most common location for a pediatric rhabdomyosarcoma, but it can occur in the oral cavity, pharynx, face and neck in the descending order of incidence. Rhabdomyosarcoma in the ear is extremely rare.   Case Report: A 5-year-old girl presented to the outpatient department of our tertiary care hospital with complaints of foul smelling, non-blood stained right ear discharge of one-month duration and deviation of angle of mouth to the left side of acute onset. Investigations revealed a diagnosis of embryonal rhabdomyosarcoma. Multimodal therapy was carried out, and the child was rendered disease-free after two years.   Conclusion: Embryonal rhabdomyosarcoma of the head and neck mimics chronic otitis media. Early diagnosis is essential to deliver prompt treatment and prevent locoregional spread and metastasis.

【 授权许可】

Unknown