Type-C esophageal atresia with double distal fistula (IIIb13)

Journal of Pediatric Surgery Case Reports

Alejandro Peñarrieta-Daher¹  Mario Peña-García²  César Ramírez-Martínez²  Jaime Nieto-Zermeño²  Cristian Zalles-Vidal³  Raúl Villegas-Silva⁴  Jaime Penchyna-Grub⁵  Karla Muñoa-Carcamo⁵  Gustavo Teyssier-Morales⁵ 

[1] Corresponding author. Hospital Infantil de México Federico Gómez, Doctor Márquez 162, Colonia Doctores, Delegación Cuauhtémoc, Ciudad de México, 06720, Mexico, .;Department of Neonatal Surgery, Hospital Infantil de México Federico Gómez, México City, Mexico;Department of Neonatology, Hospital Infantil de México Federico Gómez, México City, Mexico;Department of Pediatric Surgery, Hospital Infantil de México Federico Gómez, México City, Mexico;Department of Thoracic and Airway Surgery, Hospital Infantil de México Federico Gómez, México City, Mexico;

关键词: Esophageal atresia;    Tracheoesophageal fistula;    Bronchoesophageal fistula;    Congenital anomalies;    Double distal fistula;    Bronchoscopy;   

DOI  :  

来源: DOAJ

【 摘 要 】

Esophageal atresia (EA) is the most frequent congenital anomaly of the esophagus. According to Gross Classification, type-C esophageal atresia is the most common type. The Atlas of Esophageal Atresia by Kluth describes multiple variations of defects in EA. We present a female baby of 36 weeks’ gestation, with IIIb13 esophageal atresia, an extremely rare subtype of type-C EA. During pre-surgical bronchoscopy, we observed the presence of a double fistula, which was confirmed in the surgery. The first fistula between trachea and esophagus, and the second fistula between right main bronchus and esophagus, both in the distal esophagus. We made an esophageal anastomosis preserving the total length of the distal esophagus. This is the first report in over 20 years, and the third in the literature. The patient had a satisfactory evolution. After five months of follow-up the patient eats by suction only, with adequate weight gain, without suggestion of stenosis or gastroesophageal reflux.

【 授权许可】

Unknown