HRCT Diagnosis of Pleuroparenchymal fibroelastosis: Report of two cases

Radiology Case Reports

Ali Morshid¹  Amin Moshksar¹  Diana Palacio¹  Javier Villanueva-Meyer¹  Aparna Das²  Alexander G. Duarte² 

[1] Department of Diagnostic Radiology, University of Texas Medical Branch, Galveston TX 77555;Department of Internal Medicine, University of Texas Medical Branch, Galveston TX 77555;

关键词: Chest radiology;    Idiopathic interstitial pneumonia;    Pleuro parenchymal fibroelastosis;   

DOI  :  

来源: DOAJ

【 摘 要 】

Pleuroparenchymal fibroelastosis (PPFE) is a rare idiopathic interstitial pneumonia that is often underdiagnosed on computed tomography scans. The disease process involves a combination of fibrosis involving the visceral pleura and fibroelastic changes within the subpleural lung parenchyma. Although definitive diagnosis is based on pathological evaluation, this is often not feasible and pattern recognition on CT as ''definite PPFE'' or ''consistent with PPFE'' is important given that sub group of patients will undergo rapid progression with clinical deterioration.

【 授权许可】

Unknown