| Respirology Case Reports | |
| Catamenial haemoptysis in females with cystic fibrosis: a case series with review of management strategies | |
| Natalie E. West1  Kristina Montemayor1  Maria Gabriela Tupayachi Ortiz2  Raksha Jain3  Mindy Christianson4  Kubra M. Bozkanat5  Sigrid Ladores6  | |
| [1] Department of Internal Medicine Johns Hopkins University Baltimore MD USA;Department of Internal Medicine University of Miami Miami FL USA;Department of Internal Medicine University of Texas Southwestern Medical Center Dallas TX USA;Department of Obstetrics and Gynecology, Internal Medicine Johns Hopkins University Baltimore MD USA;Department of Pediatrics University of Texas Southwestern Medical Center Dallas TX USA;School of Nursing University of Alabama at Birmingham Birmingham AL USA; | |
| 关键词: Catamenial; cystic fibrosis; haemoptysis; oral contraceptive pills; thoracic endometriosis; | |
| DOI : 10.1002/rcr2.755 | |
| 来源: DOAJ | |
【 摘 要 】
Abstract Catamenial haemoptysis, the expectoration of blood during menses, has not been extensively reported in the cystic fibrosis (CF) literature. We describe four cases (age range: 25–34 years) of catamenial haemoptysis across four CF centres in the United States. These cases may represent thoracic endometriosis versus hormonal fluctuations in airway inflammation or infection resulting in bronchial artery bleeding. We identify common and nuanced management strategies including use of pro‐coagulants, hormone contraceptives, anti‐inflammatories, bronchial artery embolization, and use of the newer cystic fibrosis transmembrane conductance regulator (CFTR) modulators.
【 授权许可】
Unknown