Primary angiosarcoma of the oral cavity in a young adult

Autopsy and Case Reports

AseemMishra¹  MonikaGupta¹  Bhagat SinghLali²  ZachariahChowdhury² 

[1] Homi Bhabha Cancer Hospital, Department of Head and Neck Oncology;Homi Bhabha Cancer Hospital, Department of Pathology;

关键词: Maxilla;    Oral Ulcer;    Rare Diseases;    Sarcoma;   

DOI  :  

来源: DOAJ

【 摘 要 】

Angiosarcoma is a rare neoplasm, constituting only 2% of all the soft tissue tumors and most frequently involves the skin of the head and neck region in elderly males. They are extremely aggressive tumors with high rates of metastasis and poor outcomes. We report a unique case of angiosarcoma involving an unusual site – upper alveolus and maxilla in a young patient highlighting the diagnostic challenges in such a scenario. A 29 years old female presented with a non-healing wound of the oral cavity, which had progressed to the current maximum size of 6.4 cm within one month. Magnetic resonance imaging (MRI) scan revealed the involvement of maxilla up to the floor of the orbit and adjacent soft tissue. However, no distant metastasis was detected on Positron Emission Tomography (PET) scan. Biopsy of the lesion showed an irregular, highly pleomorphic, and mitotically active epithelioid soft tissue tumor conclusively diagnosed as angiosarcoma.

【 授权许可】

Unknown