Effect of dietary regime on metabolic control in phenylketonuria: Is exact calculation of phenylalanine intake really necessary?

Molecular Genetics and Metabolism Reports

Stefanie Rosenbaum-Fabian¹  Monika Jörg-Streller²  Frauke Lang³  Holger Blessing⁴  Carmen Rohde⁵  Skadi Beblo⁵  Alena Gerlinde Thiele⁵  Sabine Matzken⁶  Uta Meyer⁷  Ulrike Och⁸  Katrin Schönherr⁹  Cornelia Maddalon^1,10 

[1] Center of Pediatrics and Adolescent Medicine, University Hospital, Department of Pediatrics, Hugstetter Straße 55, 79106 Freiburg, Germany;Clinic for Pediatrics I, Inherited Metabolic Disorders, Medical University Innsbruck, Anichstrasse 35, 6020 Innsbruck, Austria;Departement of Pediatric and Adolscent Medicine, Villa Metabolica, University Medical Center, Johannes Gutenberg-University of Mainz, Langenbeckstr. 1, 55131 Mainz, Germany;Department for Inborn Metabolic Diseases, Children's and Adolescents' Hospital, University of Erlangen-Nürnberg, Loschgestraße 15, 91054 Erlangen, Germany;Hospital for Children and Adolescents, Department of Women and Child Health, University Hospitals, University of Leipzig, Liebigstraße 20 a, 04103 Leipzig, Germany;Justus Liebig University, Department for General Pediatrics, Metabolic Unit, Rudolf-Buchheim-Straße, 35392 Giessen, Germany;Medical School Hannover, Clinic of Pediatrics, Carl-Neuberg-Straße 1, 30625 Hannover, Germany;Muenster University Children's Hospital, Albert-Schweitzer-Campus 1, 48149 Münster, Germany;University Children's Hospital, Department of Clinical Genetics, Centre of treatment of metabolic diseases, Kochstr. 2, 07745 Jena, Germany;University Children's Hospital, Steinwiesstrasse 75, 8032 Zürich, Switzerland;

关键词: Dietary regime;    Phenylketonuria;    Phenylalanine;    Metabolic control;    Phe-intake;   

DOI  :  10.1016/j.ymgmr.2015.09.006

来源: DOAJ

【 授权许可】

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