A case of left ventricular non-compaction associated with Wolff-Parkinson-White syndrome

IHJ Cardiovascular Case Reports

T.S. Sirisena¹  H.G.W.A.P.L. Bandara²  A. Jegavanthan³  M. Lekamwattage³  N.M.T.C. Jayasekara³  S.R. Jayawickreme³  T. Kogulan³  D.S. Gunawardhane³  A. Kularatne³  W.M.G. Weerakoon³ 

[1]Teaching Hospital Kandy, Sri Lanka

[2]Corresponding author. Cardiology Unit, Teaching Hospital Kandy, Williyam Gopallawa Mawatha, Kandy 20000, Sri Lanka.

[3]Teaching Hospital Kandy, Sri Lanka

关键词: Left ventricular non-compaction;    Congestive heart failure;    Wolff-Parkinson-White syndrome;   

DOI  :  

来源: DOAJ

【 摘 要 】

Left ventricular non-compaction (LVNC) cardiomyopathy is a rare form of a primary cardiomyopathy with strong genetic background and the diagnosis is often challenging since this morphological trait can be shared by different conditions with varying degree of rare associations. Here we report a case of LVNC and Wolff-Parkinson-White (WPW) syndrome in a young person having a strong family history of congenital heart disease. A 33-year-old gentleman presented with episodic palpitations and syncopal attacks over one month duration. Physical examination was found to be normal. Electrocardiograph of the patient showed WPW type B pattern and the Holter monitoring study showed the evidence of paroxysmal atrial fibrillation. Transthoracic 2D echocardiography revealed mild left-ventricular dysfunction (2D biplane ejection fraction of 40%) and Global Longitudinal Strain of −15.4 with an enlarged left ventricle. Addition to that he full filled the echocardiographic criteria for LVNC cardiomyopathy. Subsequent Cardiovascular-Magnetic Resonance confirmed the diagnosis of LVNC. He was subjected for successful radio frequency ablation of the accessory pathway and started on lifelong low dose aspirin to prevent thromboembolic complications. He became symptom free following the intervention and regular echocardiographic follow-up with anti-failure treatment was established.

【 授权许可】

Unknown