Soft tissue huge solitary neurofibroma in the sacral region without neurofibromatosis: a pediatric case report

PAMJ Clinical Medicine

Dorra Daly¹  Moncef Mokni²  Khaled Sakly²  Fethi Derbel³  Mohamed Azzaza⁴  Meriem Braiki⁵ 

[1] Basic Center Health, Sidi Bouzid, Tunisia;Department of Pathology, Farhat Hached Hospital, Sousse, Tunisia;Department of Surgery, Clinique Les Olivier, Sousse, Tunisia;Department of Surgery, Sahloul University Hospital, Sousse, Tunisia;Department of Surgery, Sidi Bouzid Regional Hospital, Sidi Bouzid, Tunisia;

关键词: neurofibromas;    soft tissue;    surgery;    histopathology;   

DOI  :  10.11604/pamj-cm.2020.2.96.22133

来源: DOAJ

【 摘 要 】

Neurofibromas are thick and irregular benign neural sheath tumors touching the peripheral nerve and it may occur at any point along a nerve. Neurofibromas occur frequently as a neurofibromatosis manifestation and less commonly solitary, in unusual sites without neurofibromatosis. The imaging especially MRI is relatively helpful to determine radiological features necessary for the diagnosis, but the definitive diagnosis is established basing on the histopathological examination of the specimen. The primary therapeutic approach for neurofibromas is a complete surgical removal to prevent tumor recurrence. This article highlights a rare case of unusual soft tissue huge solitary neurofibroma in the sacral region without neurofibromatosis in a 12-old-girl.

【 授权许可】

Unknown