Hepatic perivascular epithelioid cell tumor: Five case reports and literature review

Asian Journal of Surgery

Xiaobo Zhang¹  Baosheng Wang¹  Zhen Liu¹  Yafei Qi²  Chuanzhuo Wang³ 

[1] Department of General Surgery, Shengjing Hospital, China Medical University, Shenyang, China;Department of Pathology, Shengjing Hospital, China Medical University, Shenyang, China;Department of Radiology, Shengjing Hospital, China Medical University, Shenyang, China;

关键词: hepatectomy;    Human Melanoma Black-45;    liver;    perivascular epithelioid cell tumor;   

DOI  :  10.1016/j.asjsur.2012.06.010

来源: DOAJ

【 摘 要 】

Perivascular epithelioid cell tumor (PEComa) is a rare tumor. Here, we present data regarding clinical presentations, diagnoses, management, and prognosis of five cases of hepatic PEComa between January 2002 and December 2008. Ultrasonography showed hyperechoic masses in all patients. Precontrast computed tomography (CT) showed that all lesions scanned were heterogeneous in density and were heterogeneously enhanced in arterial phase images. In two cases, magnetic resonance imaging showed hypointensity on T1-weighted images and hyperintensity on T2-weighted images. In enhanced scanning, lesions showed asymmetrical enhancement during arterial phase imaging. All tumors were composed of varying proportions of smooth muscle, adipose tissue, and thick-walled blood vessels, and showed positive immunohistochemical staining for Human Melanoma Black-45. All patients underwent hepatectomy, and there was no evidence of recurrence or metastasis during the follow-up period.

【 授权许可】

Unknown