Epithelioid Angiomyolipoma in a Pediatric Patient: Case Report and Review of Literature

Urology Case Reports

Louis P. Dehner¹  Robert Sherburne Figenshau²  Joseph B. Song²  Michael H. Johnson² 

[1] Department of Pathology Washington University School of Medicine, Saint Louis, MO, USA;Division of Urology, Department of Surgery, Washington University School of Medicine, Saint Louis, MO, USA;

关键词: Tuberous sclerosis complex;    Kidney;    Angiomyolipoma;    Epithelioid angiomyolipoma;   

DOI  :  10.1016/j.eucr.2014.05.008

来源: DOAJ

【 摘 要 】

We report a case of a 17-year-old girl with tuberous sclerosis complex who underwent partial nephrectomy for a newly discovered 7.5-cm renal mass subsequently determined to be an epithelioid angiomyolipoma, a rare variant of angiomyolipoma that can be confused clinically, radiographically, and pathologically for renal cell carcinoma. Proper diagnosis and treatment are critical, especially in the pediatric patient. This case report and review of literature serve at increasing the awareness of this renal tumor, with its somewhat unpredictable outcome, reviewing the pertinent literature on the topic of epithelioid angiomyolipoma in the clinical setting of tuberous sclerosis complex.

【 授权许可】

Unknown