Black-blood magnetic resonance imaging suggesting central nervous system vasculitis in moyamoya syndrome associated with systemic lupus erythematosus

Immunological Medicine

Takao Kumazawa¹  Daisuke Waki²  Rintaro Saito²  Keiichiro Kadoba²  Keisuke Nishimura²  Toshihiko Yokota²  Hiroyuki Murabe²  Tsutomu Okada³ 

[1] Department of Diagnostic Radiology, Kurashiki Central Hospital;Department of Endocrinology and Rheumatology, Kurashiki Central Hospital;Department of Radiology, Kitano Hospital, The Tazuke Kofukai Medical Research Institute;

关键词: systemic lupus erythematosus;    moyamoya syndrome;    central nervous system vasculitis;    black-blood magnetic resonance imaging;   

DOI  :  10.1080/25785826.2021.1878728

来源: DOAJ

【 摘 要 】

Moyamoya syndrome is a cerebrovascular disorder characterized by bilateral stenosis and occlusion of the internal carotid arteries and their branches. A 45-year-old woman with a history of systemic lupus erythematosus was admitted for recurrent ischemic strokes. Magnetic resonance (MR) angiography revealed moyamoya-like vasculopathy. Black-blood gadolinium-based contrast-enhanced MR images showed strong, concentric enhancement along the occluded arteries, which suggested vasculitis as the etiology of moyamoya-like vasculopathy. Intensive immunosuppressive therapy combined with anticoagulation therapy and rehabilitation led to a favorable outcome in this case. Black-blood MR imaging can be a non-invasive and prompt imaging modality when central nervous system vasculitis is suspected.

【 授权许可】

Unknown