A Rare Case of Ectopic Adrenocorticotropic Hormone Secretion from Pancreatic Neuroendocrine Tumour Presenting with Cushing Syndrome

GE: Portuguese Journal of Gastroenterology

Asmawiza Awang¹  Jasminder Sidhu²  Soon Liang Lee²  Chiun Yann Ng² 

[1] Department of Pathology, Kuala Lumpur General Hospital, Ministry of Health, Kuala Lumpur, Malaysia;Gastroenterology and Hepatology Unit, Department of Medicine, Kuala Lumpur General Hospital, Ministry of Health, Kuala Lumpur, Malaysia;

关键词: adrenocorticotropic hormone;    pancreatic neuroendocrine tumour;    cushing syndrome;   

DOI  :  10.1159/000521518

来源: DOAJ

【 摘 要 】

Ectopic adrenocorticotropic hormone secretion (EAS) from the pancreatic neuroendocrine tumour (PNET) is rare, aggressive, and challenging to treat. We hereby present a rare case of EAS from PNET presenting with Cushing syndrome diagnosed with endoscopic ultrasound-guided fine-needle aspiration cytology. This case highlights the advanced presentation of EAS from PNET with poor clinical correlation of hypercortisolism and the grade of PNET.

【 授权许可】

Unknown