Odontogenic myxofibroma of gingiva in a pediatric patient with tuberous sclerosis: A rare case report

Contemporary Clinical Dentistry

关键词: Angiofibromas;    gingival enlargement;    odontogenic myxofibroma;    tuberous sclerosis;   

DOI  :  10.4103/0976-237X.194120

来源: DOAJ

【 摘 要 】

Tuberous sclerosis complex (TSC) is a rare multisystem genetic disease, with an estimated incidence of 1 in 6000–1 in 10,000. TSC is an autosomal dominant syndrome involving heart, kidneys, lungs, and skin. The classic triad of TSC is seizures, mental retardation, and angiofibromas; this triad occurs in only 29% of patients. The clinical diagnostic guidelines on TSC are prepared based on clinical features, radiographic findings. The most common oral manifestations of TSC are fibroma, gingival hyperplasia, and enamel hypoplasia. Odontogenic myxofibroma represents a rare slow-growing benign neoplasm found rarely in children below 10 years or adults over 50 years of age. The prevalence of myxoma is between 0.04% and 3.7%. Here, we are reporting a rare case of myxofibroma of gingiva in an 8-year-old female TSC patient.

【 授权许可】

Unknown