Breast location of Darier and Ferrand dermatofibrosarcoma: a rare case report

PAMJ Clinical Medicine

Karima Mouden¹  Afaf Semmar¹  Soukaina Wakrim² 

[1] Department of Radiation Oncology, National Oncology Institute, Rabat, Morocco;Department of Radiology, Ibn Zohr University, Faculty of Medicine and Pharmacy, Agadir, Morocco;

关键词: breast;    darier and ferrand dermatofibrosarcoma;    wide excision;   

DOI  :  10.11604/pamj-cm.2019.1.43.21049

来源: DOAJ

【 摘 要 】

Darier and Ferrand Dermatofibrosarcoma (DFS) is a very uncommon pathology type of skin cancer. Breast location remains very rare, with only dozens of cases reported to date in the English literature. We report the case of a 21-year-old woman who presented with a left breast mass that had been present for more than 4 years. Clinical examination found cutaneous mass occupying the upper internal quadrant of the left breast measuring 3 x 2cm. The patient underwent an excision of the mass with positive margin. Histological and immunohistochemical findings were suggestive of a Darier and Ferrand Dermatofibrosarcoma (DFS). In front of this clinical board, wide excision of the mass was performed. 15 months after the end of surgery, the patient was in good health, with excellent local control. The purpose of presenting this case is not only to report an uncommon pathology subtype, but mostly to provide a long-term survival of Darier and Ferrand Dermatofibrosarcoma (DFS) of breast cancer that is very rare.

【 授权许可】

Unknown