Segmental Pulmonary Hypertension in Children with Congenital Heart Disease

Medicina

BibhutiB. Das¹  Benjamin Frank²  Dunbar Ivy² 

[1] Department of Pediatric Cardiology, Baylor College of Medicine, Texas Children’s Hospital Austin Specialty Care, Austin, TX 78759, USA;Department of Pediatric Cardiology, University of Colorado Health Science Center, Children’s Hospital of Colorado, Denver, CO 80045, USA;

关键词: pulmonary hypertension in children;    congenital heart disease;    segmental pulmonary hypertension;    digital subtraction angiography;   

DOI  :  10.3390/medicina56100492

来源: DOAJ

【 摘 要 】

Segmental pulmonary hypertension is a complex condition in children that encompasses many congenital heart diseases including pulmonary atresia with ventricular septal defect, hemitruncus/truncus arteriosus with branch pulmonary artery stenosis, unilateral absent pulmonary artery, and several post-tricuspid shunt lesions. Multimodality imaging is required to confirm and assess pulmonary vascular disease in subjects with major aorto-pulmonary collaterals. We describe 3 children with complex congenital heart defects who have a variable degree of segmental pulmonary hypertension and discuss management strategies and the role of interventional and/or pulmonary hypertension targeted therapies.

【 授权许可】

Unknown