Perioperative management of a patient with Xeroderma Pigmentosum: A case report

Journal of Pediatric Surgery Case Reports

Debnath Chatterjee¹  Leah M. Webb²  Megan A. Brockel³ 

[1] Department of Anesthesiology, Children's Hospital Colorado, University of Colorado School of Medicine, Aurora, CO, USA;Corresponding author. 13123 E 16th Ave, Box 090, Aurora, CO, 80045, USA.;Department of Anesthesiology, Children's Hospital Colorado, University of Colorado School of Medicine, Aurora, CO, USA;

关键词: Xeroderma pigmentosum;    UV radiation;    Pediatric airway management;   

DOI  :  

来源: DOAJ

【 摘 要 】

Perioperative care of patients with Xeroderm Pigmentosum (XP), a rare disorder of DNA repair [1,2], presents many anesthetic challenges. Firstly, harmful ultraviolet radiation can be detected in perioperative areas. Also, anesthetic type must be carefully considered, as exposure to volatile anesthetics may hasten the development of neurodegeneration (Masuda et al., 2002; Reitz and Lanz, 1993; Miyazaki et al., 2007; Fjouji et al., 2013) [3-6]. Furthermore, muscle relaxants can produce a prolonged effect (Soen et al., 2006) [7]. Airway management may be difficult secondary to skin changes and growths (Zarrouki et al., 2017; Hajijafari et al., 2014; Meyer, 1982) [8-10]. Even the risk of using imaging modalities should be considered. Given the above exposure risks, we present considerations for preparing to care for patients with XP in the perioperative period and information on where to purchase supplies to prepare the perioperative area.

【 授权许可】

Unknown