Para aortic ganglioneuroma presenting as Cushing′s syndrome

Indian Journal of Urology

关键词: Cushing′s syndrome;    ectopic ACTH;    ganglioneuroma;    para aortic;   

DOI  :  10.4103/0970-1591.36725

来源: DOAJ

【 摘 要 】

We present a case of an eight-year-old female presenting with four months history of progressive weight gain, short stature, obesity, mild acanthosis, moon facies and buffalo hump. Biochemically, low-dose and high-dose Dexamethasone tests were not suppressible, ACTH was raised and 24h urinary metanephrines were normal. The CECT scan showed a 3cm paraganglioma. Tumor was excised via 11 th rib transcostal approach and the mass was found arising from the sympathetic chain. Histopathology was suggestive of ganglioneuroma positive for ACTH immunostaining.

【 授权许可】

Unknown