A single coronary artery with left circumflex artery crossing right ventricular outflow tract in tetralogy of Fallot with absent left pulmonary artery

Journal of Cardiovascular and Thoracic Research

卷:13

Dheemta Toshkhani¹  Ganesh Kumar Munirathinam¹  Vivek Jaswal²  Vikas Kumar²  Ruchit Patel²  Shyam Kumar Singh Thingnam² 

[1] Department of Anaesthesia and Critical Care, Post Graduate Institute of Medical Education and Research (PGIMER), Chandigarh, India;

[2] Department of Cardiovascular and Thoracic Surgery, Post Graduate Institute of Medical Education and Research (PGIMER), Chandigarh, India;

关键词: single coronary artery;    left circumflex artery;    right ventricular outflow tract;    tetralogy of fallot;    absent left pulmonary artery;   

DOI  :  10.34172/jcvtr.2020.61

来源: DOAJ

【 摘 要 】

Tetralogy of Fallot (TOF) with unilateral absence of pulmonary artery and the anomalous coronary artery is a rare combination. Detailed preoperative evaluation of coronary artery anatomy is must to prevent injury to the major vessels crossing right ventricular outflow tract. We report a rare association of single coronary artery with left circumflex artery crossing right ventricular outflow tract close to the pulmonary annulus in tetralogy of Fallot with absent left pulmonary artery in 11-year-old girl. Though there is a great diversity of coronary anomalies in tetralogy of Fallot, the prepulmonic course of left circumflex artery crossing the right ventricular outflow tract (RVOT) close to the pulmonary annulus has rarely been described in the literature. The patient underwent successful primary single lung intracardiac repair. Right ventricular outflow tract obstruction was treated by handmade valved pericardial autologous conduit and release of the tethering of hypoplastic native unicuspid pulmonary valve leaflet maintaining its integrity.

【 授权许可】

Unknown