Morphological Adaptation after Bilateral Lung Transplantation in a Patient with Kartagener Syndrome: A Case Report

Journal of Chest Surgery

卷:55

Bong Soo Son¹  Joohyung Son¹  Do Hyung Kim¹  Chang Hun Kim¹ 

[1] Medical Research Institute of Pusan National University;

关键词: kartagener syndrome;    situs inversus totalis;    lung transplantation;    case report;   

DOI  :  10.5090/jcs.21.086

来源: DOAJ

【 摘 要 】

Kartagener syndrome (KS) is a rare disease with an incidence of 1 in 20,000 to 30,000 births.There is no cure for KS, and conservative medical treatments are used to relieve symptomsand prevent disease progression. Lung transplantation (LT) is the only treatment optionfor end-stage KS. Since patients with KS have anatomical abnormalities such as situs inversustotalis, which often require surgery to correct, most reports are related to surgicaltechniques. Reports about morphological adaptations and changes in transplanted lungstructure after LT in patients with KS are rare. We performed LT in a patient with KS andobserved morphological adaptation of the lungs for 6 months on chest computed tomographyusing a quantitative evaluation tool (Chest Image Platform; Harvard UniversityDisability Resources, Cambridge, MA, USA).