A large undifferentiated sarcoma of the liver in a 13-year-old girl treated with anatomical resection: a case report and review of the literature

BMC Gastroenterology

Ali Bahador¹  Mehdi Forooghi¹  Maryam Ataollahi²  Bita Geramizadeh³  Hooman Kamran⁴  Reza Shahriarirad⁵ 

[1] Department of Pediatric Surgery, Nemazee Hospital, Shiraz University of Medical Sciences, Shiraz, Iran;Gastroenterohepatology Research Center, Shiraz University of Medical Sciences, Shiraz, Iran;Shiraz Transplant Research Center (STRC), Shiraz University of Medical Sciences, Shiraz, Iran;Department of Pathology, Shiraz University of Medical Sciences, Shiraz, Iran;Student Research Committee, Shiraz University of Medical Sciences, Shiraz, Iran;Nemazee Hospital, Zand Street, Nemazee Square, 71936-13311, Shiraz, Iran;Student Research Committee, Shiraz University of Medical Sciences, Shiraz, Iran;Thoracic and Vascular Surgery Research Center, Shiraz University of Medical Sciences, Shiraz, Iran;

关键词: Undifferentiated embryonal sarcoma;    UESL;    Hepatectomy;    Liver resection;    Malignant liver tumor;   

DOI  :  10.1186/s12876-021-02076-x

来源: Springer

【 摘 要 】

BackgroundUndifferentiated embryonal sarcoma of the liver (UESL) is a rare liver tumor accounting for 6–13% of primary liver tumors. Accurate preoperative diagnosis is difficult, with a rather high misdiagnosis rate. Herein, we reported a very large UESL treated with anatomical resection. Our case is amongst the largest pediatric UESLs in the literature.Case presentationHerein, we report a 13-year-old girl presenting with right upper quadrant abdominal pain, postprandial vomiting, and abdominal distention, in which radiographic imaging demonstrated a huge UESL (28 × 20 × 12 cm). The patient was treated with partial hepatectomy and the 5 kg tumor was removed. The patient was discharged in good condition, with no significant complaints in her follow-up.ConclusionsAlthough different treatment strategies have been reported for UESL cases, anatomical resection is still the main treatment approach, especially for large tumors.

【 授权许可】

CC BY