Hepatic inflammatory pseudotumor-like follicular dendritic cell tumor: a case report

Journal of Medical Case Reports

Cezar Iulian Bețianu¹  Ana Daniela Pascariu²  Andrei Valentin Neagu²  Alexandru Băjenaru²  Andreea Ioana Neagu² 

[1] Department of Interventional Radiology, “Carol Davila” Central Military Emergency University Hospital, Mircea Vulcanescu Street, no.88, 010825, Bucharest, Romania;Department of Radiology, “Carol Davila” Central Military Emergency University Hospital, Mircea Vulcanescu Street, no. 88, 010825, Bucharest, Romania;

关键词: Epstein–Barr virus;    Follicular dendritic cell sarcoma;    Hepatic tumor;    Inflammatory pseudotumor;    Case report;   

DOI  :  10.1186/s13256-021-02957-5

来源: Springer

【 摘 要 】

BackgroundInflammatory pseudotumor-like follicular dendritic cell sarcoma is a rare histological variant of follicular dendritic cell sarcoma involving typically the spleen and the liver, often linked to the presence of Epstein–Barr virus infection. Definite diagnosis of this type of sarcoma is difficult to make owing to nonspecific clinical and imaging findings and is based on histopathological features. Inflammatory pseudotumor-like follicular dendritic cell sarcoma is described as a low-aggressivity tumor with a favorable prognosis.Case presentationWe report the case of a 34-year-old Caucasian woman, Epstein–Barr virus positive, diagnosed with hepatic inflammatory pseudotumor-like follicular dendritic cell sarcoma and surgically treated in November 2014, who developed 6 years later a recurrence for which she underwent once again surgical treatment. As far as we know, fewer than 30 reports of inflammatory pseudotumor-like follicular dendritic cell liver tumors have been reported in the English literature.ConclusionsAlthough it is an uncommon tumor, inflammatory pseudotumor-like sarcoma is a diagnostic worth being taken in consideration, and surveillance is recommended owing to the possibility of recurrence.

【 授权许可】

CC BY