Massive hemothorax in a pregnant patient with neurofibromatosis type 1

Journal of Cardiothoracic Surgery

Akira Takada¹  Takayuki Fukui²  Kumiko Hashimoto³  Yuji Nomata³  Kunio Narita³ 

[1] Department of Radiology, Toyohashi Municipal Hospital, Toyohashi, Aichi, Japan;Department of Thoracic Surgery, Nagoya University, Nagoya, Japan;Department of Thoracic Surgery, Toyohashi Municipal Hospital, 50 Hachiken-nishi, Aotake-cho, 441-8570, Toyohashi, Aichi, Japan;

关键词: Hemothorax;    Pregnancy;    Emergency;   

DOI  :  10.1186/s13019-021-01504-z

来源: Springer

【 摘 要 】

BackgroundReports of spontaneous hemothorax in patients with neurofibromatosis type 1 are scarce despite the severe complication. We herein present the first case of hemothorax in a neurofibromatosis type 1 patient during pregnancy and discuss the difficulty associated with its diagnosis and treatment.Case presentationA 39-year-old female at 34 weeks gestation presented with sudden left back pain and dyspnea. Chest radiography revealed massive left pleural effusion. Computed tomography showed bleeding from the intercostal artery. Although the patient appeared hemodynamically stable, the fetus was in a critical condition. Emergency caesarean section was performed within 1 hour. Subsequently, we performed endovascular coil embolization of the intercostal artery. While this intensive treatment saved the patient, her fetus could not be rescued.ConclusionsPatients with neurofibromatosis type 1 may develop massive hemothorax without gross lesions. In late pregnancy, sufficient infusion and quick hemostasis are essential and can be lifesaving.

【 授权许可】

CC BY