Congenital Cystic Adenomatoid Malformation with Bronchial Atresia in Elderly Patients

Tuberculosis and Respiratory Diseases

article

Hyun Jung Kwak¹  Ji-Yong Moon²  Sa-Il Kim¹  Tae Hyung Kim¹  Jang Won Sohn¹  Sang-Heon Kim¹  Dong Ho Shin¹  Sung Soo Park¹  Won Sang Chung³  Ho Joo Yoon¹ 

[1] Department of Internal Medicine, Hanyang University College of Medicine;Department of Internal Medicine, Medical Foundation Hanil General Hospital;Department of Thoracic and Cardiovascular Surgery, Hanyang University College of Medicine

关键词: Cystic Adenomatoid Malformation of Lung;    Congenital;    Aged;    Bronchi;    Abnormalities;   

DOI  :  10.4046/trd.2012.72.6.501

学科分类：医学（综合）

来源: The Korean Academy of Tuberculosis and Respiratory Diseases

【 摘 要 】

Congenital cystic adenomatoid malformation (CCAM) is an uncommon, nonhereditary anomaly caused by arrest of lung. Patients with CCAM may present with respiratory distress as newborns, or may remain asymptomatic until later in life. CCAM type I is rarely found in association with bronchial atresia (BA) in adults; we present such a case. Case: A 54-year-old female presented with chronic cough and blood-tinged sputum. Physical examination and laboratory tests were unremarkable. Chest radiographs and a CT scan of the chest showed multiple large air-filled cysts consistent with a CCAM in the right lower lobe, and an oval-shaped opacity in the distal right middle lobal bronchus. Based on the radiologic findings, right middle lobectomy and a medial basal segmentectomy of the right lower lobe were performed via a thoracotomy. These lesions were consistent with Stocker's Type I CCAM and BA in the different lobes.

【 授权许可】

CC BY-NC