Multicentric angiomyolipoma in kidney, liver, and lymph node: case report/review of the literature

Jornal Brasileiro de Patologia e Medicina Laboratorial

Artur S. De Azevedo¹  Nábia Maria M. S. Simão¹ 

关键词: angiomyolipoma;    tuberous sclerosis;    perivascular epithelioid cell neoplasms;    angiomiolipoma;    esclerose tuberosa;    neoplasia de células epitelioides perivasculares;   

DOI  :  10.5935/1676-2444.20150030

来源: SciELO

【 摘 要 】

ABSTRACT Introduction: The angiomyolipoma (AML) is constituted by adipose tissue, blood vessels and smooth muscle fiber; follows a benign clinical course, with slow growth and absence of metastasis, occurring in tuberous sclerosis or sporadically. Objective: We intend to describe the clinical, radiological and histological aspects of this tumor. Case report: A-64-year-old woman presented with abdominal pain and dyspepsia. Tomography showed hepatic, renal and mesenteric nodules. Histological evaluation of mesenteric lymph node revealed perivascular epithelioid differentiation neoplasia, compatible with AML/perivascular epithelioid cell tumor (PEComa), positive for anti-S100, anti-human melanoma black-45 (HMB-45) and anti-smooth muscle actin. Conclusion: We described a rare AML with renal, hepatic and lymph node involvement, representing a multicenter version instead of metastasis.

【 授权许可】

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