Multicentric pheochromocytoma and involvement of the inferior vena cava

Sao Paulo Medical Journal

Antonio Marmo Lucon¹  Renato Falci Júnior¹  José Nery Praxedes¹  Marcel Cerqueira Cesar Machado¹  Luis Balthazar Saldanha¹  Marcelo Marcondes Machado¹  Sami Arap¹ 

[1] ,Universidade de São Paulo Faculty of Medicine Hospital das ClínicasSão Paulo,Brazil

关键词: Pheochromocytoma;    Retroperitoneal neoplasia;    Adrenal tumor;    Adrenal surgery;    Vena cava;    Feocromocitoma;    Neoplasia retroperitoneal;    Tumor adrenal;    Veia cava;   

DOI  :  10.1590/S1516-31802001000200010

来源: SciELO

【 摘 要 】

CONTEXT: Extension of pheochromocytomas to the inferior vena cava is rare. Multicentric tumors are rare as well, being present in up to 10% of cases. Surgery is the treatment of choice because of the long-term survival free of disease. DESIGN: Case report. CASE REPORT: We report on a case of right adrenal pheochromocytoma with extension to the supra-diaphragmatic vena cava, which underwent surgical excision through thoracophrenic laparotomy without the need for cardiopulmonary bypass. In a 6-year follow-up, another pheochromocytoma was found in the infra-renal Zuckerkandl's organ. Complete surgical excision of the tumor was performed by a median laparotomy and complete retroperitoneal dissection. In both cases, the total removal of the pheochromocytoma has been guaranteed by having margins free of tumor and a normal post-operative level of catecholamines. The pathological study revealed a malignant pheochromocytoma with margins free of neoplasia in both specimens.

【 授权许可】

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