Granulomatosis with polyangiitis, a new nomenclature for Wegener's Granulomatosis - Case report

Anais Brasileiros de Dermatologia

Alexandre Moretti De Lima¹  Pedro De Freitas Silva Torraca¹  Sheila Pereira Da Rocha¹  Carmelia Matos Reis Santiago¹  Fabio Humberto Ribeiro Paes Ferraz¹ 

关键词: Anti-neutrophil cytoplasmic antibody-associated vasculitis;    Granulomatosis with Polyangiitis;    Vasculitis;   

DOI  :  10.1590/abd1806-4841.20153455

来源: SciELO

【 摘 要 】

Abstract The granulomatosis with polyangiitis, initially known as Wegener's granulomatosis, is a small and medium vessels vasculitis. It's classic form presents a triad: necrotizing granuloma of respiratory tract, necrotizing cutaneous vasculitis and glomerulonephritis. This vasculitis has cytoplasmic antineutrophil antibodies as signal. This work illustrates a case, of multisystemic rare disease, in which the segment and treatment were considered satisfactory for symptoms remission.

【 授权许可】

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