Diffuse systemic sclerosis with bullous lesions without systemic manifestations

Anais Brasileiros de Dermatologia

Paula Renaux Wanderley Caratta Macedo¹  Amanda Nascimento Cavalleiro De Macedo Mota¹  Alexandre Carlos Gripp¹  Maria De Fatima Guimarães Scotelaro Alves¹  Evandro Mendes Klumb¹ 

关键词: Connective tissue diseases;    Scleroderma;    diffuse;    Scleroderma;    systemic;    Skin diseases;    vesiculobullous;    Skin and connective tissue diseases;    Dermatopatias vesiculobolhosas;    Doenças da pele e do tecido conjuntivo;    Doenças do tecido conjuntivo;    Esclerodermia difusa;    Escleroderma sistêmico;   

DOI  :  10.1590/abd1806-4841.20132160

来源: SciELO

【 摘 要 】

Here, we describe an atypical case of systemic sclerosis in its diffuse cutaneous form with acute and rapid progression of the cutaneous condition, without any systemic manifestations and the infrequent formation of bullae, showing the importance of diagnosis and early treatment in such cases. This case also shows that special measures should be taken for bullous cutaneous lesions and ulcerations resulting from serious sclerosis, which are entry points and increase morbidity and risk of death. Other prognostic factors include age, ESR and renal and pulmonary involvement. Capillaroscopies can be useful predictors of greater severity of systemic scleroderma, revealing a greater link with systemic, rather than cutaneous, involvement.

【 授权许可】

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