Graham-Little Piccardi Lassueur Syndrome: case report

Anais Brasileiros de Dermatologia

Raquel Bissacotti Steglich²  Renata Elise Tonoli¹  Giselle Martins Pinto²  Fernanda Melo Müller²  Isabelle Maffei Guarenti²  Ernani Siegmann Duvelius² 

[1] ,Charity Hospital of Porto Alegre Dermatology Service Porto Alegre RS ,Brazil

关键词: Alopecia;    Hypotrichosis;    Lichen planus;    Alopecia;    Hipotricose;    Líquen plano;   

DOI  :  10.1590/S0365-05962012000500019

来源: SciELO

【 摘 要 】

A 33-year-old woman presented with a 3-year history of progressive alopecia of the scalp. Past treatment with hydroxicloroquine did not show improvement. Physical examination revealed multiple areas of alopecia with atrophic aspect of the scalp, and axillary and pubic hypotrichosis. Dermoscopy showed hyperkeratosis and accentuation of follicular ostia. Anatomopathological examination revealed decrease in the number of hair follicles, upper perifollicular infiltrate and areas with fibrosis. The Piccardi-Lassueur-Graham-Little syndrome is a rare disorder, characterized by the triad of multifocal scarring alopecia of the scalp, keratotic follicular eruption and hypotrichosis of axillary and pubic regions. Management is a challenge and many medications tried have controversial results. We report a case of this rare syndrome which improved with corticoids.

【 授权许可】

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