A case of late-onset oligomeganephronia

Jornal Brasileiro de Nefrologia

Rafael José Vargas Alves²  Kenselyn Oppermann¹  Luiz Eduardo Schein¹  Karla Lais Pêgas² 

[1] ,Santa Casa de Misericórdia de Porto Alegre

关键词: congenital abnormalities;    kidney failure;    chronic;    proteinuria;    anormalidades congênitas;    insuficiência renal crônica;    proteinúria;   

DOI  :  10.5935/0101-2800.20120030

来源: SciELO

【 摘 要 】

A 33-year old caucasian man was investigated for pain in the right flank, proteinuria, hemathuria and an elevated serum creatinine level. He also presented an abnormal ultrasonography, which revealed asymmetric kidneys. Through renal biopsy, the diagnosis of oligomeganephronia (OMN) was confirmed. OMN is a very rare form of renal hypoplasia, and late-onset in adulthood is even rarer. In the pediatric population, OMN leads to end-stage-renal-failure(ESRF) in a few years. This is the sixth case related in the literature of a late-onset OMN who have not yet developed ESRF.

【 授权许可】

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