期刊论文详细信息
Radiologia Brasileira | |
Cleidocranial dysostosis: a report on two familial cases | |
Carlos Guilherme Gaelzer Porciuncula1  Ricardo Ferreira De Lira1  Maria Lúcia Lima Soares1  Diego Lisboa Araújo1  Lucas Rocha Mota1  Larine Ferreira Lira1  | |
关键词: Cleidocranial dysplasia; Hypoplasia of clavicles; Supernumerary teeth; Disostose cleidocraniana; Hipoplasia de clavícula; Dentes extranumerários; | |
DOI : 10.1590/S0100-39842013000600013 | |
来源: SciELO | |
【 摘 要 】
Cleidocranial dysostosis is a rare genetic syndrome with an autosomal dominant inheritance pattern. The most common manifestations include clavicular aplasia or hypoplasia, open fontanelles and abnormal dentition. The present report describes two familial cases whose late diagnosis was made by means of clinical and radiographic findings. The treatment was radical, with complete surgical teeth extraction and making of total dental prosthesis.
【 授权许可】
CC BY
All the contents of this journal, except where otherwise noted, is licensed under a Creative Commons Attribution License
【 预 览 】
Files | Size | Format | View |
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RO202005130060148ZK.pdf | 144KB | download |