Current issues in the respiratory care of patients with amyotrophic lateral sclerosis

Arquivos de Neuro-Psiquiatria

Marco Orsini¹  Agnaldo José Lopes¹  Sara Lucia Silveira De Menezes¹  Acary Bulle Oliveira¹  Marcos Raimundo Gomes De Freitas¹  Osvaldo Jose Moreira Do Nascimento¹  Fernando Silva Guimarães¹ 

关键词: amyotrophic lateral sclerosis;    respiratory function;    rehabilitation;    esclerose lateral amiotrófica;    função respiratória;    reabilitação;   

DOI  :  10.1590/0004-282X20150132

来源: SciELO

【 摘 要 】

Amyotrophic lateral sclerosis is a progressive neuromuscular disease, resulting in respiratory muscle weakness, reduced pulmonary volumes, ineffective cough, secretion retention, and respiratory failure. Measures as vital capacity, maximal inspiratory and expiratory pressures, sniff nasal inspiratory pressure, cough peak flow and pulse oximetry are recommended to monitor the respiratory function. The patients should be followed up by a multidisciplinary team, focused in improving the quality of life and deal with the respiratory symptoms. The respiratory care approach includes airway clearance techniques, mechanically assisted cough and noninvasive mechanical ventilation. Vaccination and respiratory pharmacological support are also recommended. To date, there is no enough evidence supporting the inspiratory muscle training and diaphragmatic pacing.

【 授权许可】

CC BY   
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