Status dystonicus: study of five cases

Arquivos de Neuro-Psiquiatria

Hélio A.g. Teive²  Renato P. Munhoz²  Mônica M. Souza¹  Sérgio A. Antoniuk¹  Mara Lucia S.f. Santos¹  Manoel Jacobsen Teixeira¹  Egberto Reis Barbosa¹  Rodrigo C. Carvalho¹  Milberto Scaff¹  Lineu César Werneck² 

[1] ,Universidade Federal do Paraná Hospital de Clínicas Serviço de NeurologiaCuritiba PR ,Brasil

关键词: status dystonicus;    dystonic storm;    dystonia;    status dystonicus;    tempestade distônica;    distonia;   

DOI  :  10.1590/S0004-282X2005000100005

来源: SciELO

【 摘 要 】

Status Dystonicus (SD) is characterized by generalized muscle contractions in dystonic patients. We report 5 cases of SD, two of which in patients with dystonic cerebral palsy, one in a patient with primary segmental dystonia, one in a patient with Hallervorden-Spatz syndrome and one in a patient with Wilson's disease (WD). Three patients were admitted to an intensive care unit and treated with propofol and midazolam, and two were submitted to neurosurgical procedures (bilateral pallidotomy and bilateral pallidal deep brain stimulation). Triggering factors were identified in three patients as follows: infection, stress-induced and zinc therapy for WD. On follow-up, two patients presented with significant improvement of dystonia, whereas the other three cases the clinical picture ultimately returned to baseline pre-SD condition.

【 授权许可】

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