Axoval neuropathy as initial manifestation of primary amyloidosis: report of a case submitted to bone marrow transplantation

Arquivos de Neuro-Psiquiatria

Orlando G. Povoas Barsottini¹  Adriano Arantes¹  Daniel Sigulem¹  José Mauro Kutner¹  Andreza Alice Feitosa Ribeiro¹  Luiz A. Moura¹  Nelson Hamerschlak¹ 

[1] ,Hospital Israelita Albert Einstein Instituto de Ensino e Pesquisa Albert Einstein São Paulo SP ,Brazil

关键词: amyloid neuropathies;    amyloidosis;    autologous bone marrow transplantation;    autologous transplantation;    neuropatias amilóide;    amiloidose;    transplante autólogo de medula óssea;    transplante autólogo;   

DOI  :  10.1590/S0004-282X2004000400030

来源: SciELO

【 摘 要 】

Amyloidosis is a syndrome characterized by deposition of a highly insoluble protein material in the extracellular space that may affect several organs. It may be generalized and idiopathic (primary amyloidosis). We describe the case of a 48 years-old woman with axonal neuropathy associated with proteinuria, whose final investigation resulted in diagnosis of primary amyloidosis (AL). She was submitted to autologous bone marrow transplantation. We discuss some aspects related to diagnosis of neuropathy and current treatment of AL.

【 授权许可】

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