MR and CT imaging in the Dyke-Davidoff-Masson syndrome: report of three cases and contribution to pathogenesis and differential diagnosis

Arquivos de Neuro-Psiquiatria

Paulo Henrique Aguiar²  Wei Liu Ching¹  Helio LeitÃo¹  F. Issa²  Guilherme Lepski²  Eberval Gadelha Figueiredo²  Fernando Gomes-pinto²  Raul Marino Jr² 

[1] ,University of São Paulo Medical School Hospital das Clínicas Department of NeurologySão Paulo,Brazil

关键词: Dyke-Davidoff-Masson syndrome;    brain atrophy;    computerized tomography;    magnetic resonance image;    síndrome de Dyke-Davidoff-Masson;    atrofia cerebral;    tomografia computadorizada;    ressonância magnética;   

DOI  :  10.1590/S0004-282X1998000500016

来源: SciELO

【 摘 要 】

Cerebral hemiatrophy or Dyke-Davidoff-Masson syndrome is a condition characterized by seizures, facial asymmetry, contralateral hemiplegia or hemiparesis, and mental retardation. These findings are due to cerebral injury that may occur early in life or in utero. The radiological features are unilateral loss of cerebral volume and associated compensatory bone alterations in the calvarium, like thickening, hyperpneumatization of the paranasal sinuses and mastoid cells and elevation of the petrous ridge. The authors describe three cases. Classical findings of the syndrome are present in variable degrees according to the extent of the brain injury. Pathogenesis is commented.

【 授权许可】

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