Rhegmatogenous retinal detachment in Wyburn-Mason syndrome: case report

Arquivos Brasileiros de Oftalmologia

Flávio Maccord Medina²  Otacílio De Oliveira Maia Júnior¹  Walter Yukihiko Takahashi¹ 

[1] ,Universidade do Estado do Rio de Janeiro Department of Ophthalmology Rio de Janeiro RJ ,Brazil

关键词: Arteriovenous malformations;    Arteriovenous malformations;    Retinal detachment;    Vitreous hemorrhage;    Intracranial arteriovenous malformations;    Intracranial arteriovenous malformations;    Retinal artery;    Retinal vein;    Syndrome;    Case reports;    Malformações arteriovenosas;    Malformações arteriovenosas;    Descolamento retiniano;    Hemorragia vítrea;    Malformações arteriovenosas intracranianas;    Malformações arteriovenosas intracranianas;    Artéria retiniana;    Veia retiniana;    Síndrome;    Relatos de casos;   

DOI  :  10.1590/S0004-27492010000100017

来源: SciELO

【 摘 要 】

Wyburn-Mason is a rare vascular disorder, comprised of arteriovenous malformations (AVMs) of the midbrain and retina. It can cause visual symptoms depending on its localization and extension. Vitreous and intraretinal hemorrhage and neovascular glaucoma have been previously described. A case of rhegmatogenous retinal detachment in a patient with Wyburn-Mason syndrome is described. A 27 year-old woman previously diagnosed with Wyburn-Mason syndrome, sought attendance with sudden low vision in right eye 3 months before. She presented moderate vitreous hemorrhage and retinal detachment with a superior tear. She underwent a successful posterior vitrectomy with implantation of silicone oil, with reattachment of the retina. Rhegmatogenous retinal detachment in a patient with Wyburn-Mason syndrome has been not previously described in the literature. Vitrectomy in this case present challenges related to intraoperatory bleeding risk, to a posterior pole tear among AVMs and the difficulty of obtaining free retina for photocoagulation.

【 授权许可】

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