Surgical Treatment of Intra-Abdominal Desmoid Tumors Resulting In Short Bowel Syndrome

Cancers

Matthew Wheeler¹  David Mercer¹  Wendy Grant¹  Jean Botha¹  Alan Langnas¹ 

[1]Department of Surgery, University of Nebraska Medical Center, The Nebraska Medical Center 3280, Omaha, NE 68198, USA

关键词: intra-abdominal desmoid tumors;    short bowel syndrome;    familial adenomatous polyposis;   

DOI  :  10.3390/cancers4010031

来源: mdpi

【 摘 要 】

Advanced intra-abdominal desmoids tumors present with severe symptoms, complications or rapid growth, which lead to adverse outcomes. Our aim was to evaluate the treatment and outcome of patients with advanced intra-abdominal desmoids tumors, and develop guidelines for surgical management of these patients. We reviewed the clinical courses of 21 adult patients with advanced stage intra-abdominal desmoid tumors who presented to an intestinal rehabilitation and transplantation program. Patients with massive intestinal resection presented in two groups. The first group had a short small intestinal remnant after resection (<60 cm). These patients were poor rehabilitation candidates and eventually met criteria for transplant. The second had longer intestinal remnants and were more successfully rehabilitated and have not had complications that would lead to transplantation. Advanced intra-abdominal desmoid tumors have outcomes after resection that merit aggressive resection and planned intestinal rehabilitation and intestinal transplantation as indicated.

【 授权许可】

CC BY   
© 2012 by the authors; licensee MDPI, Basel, Switzerland.