Idiopathic hypereosinophilic syndrome: a rare cause of erythroderma

Journal of Dermatological Case Reports

Karaninder S. Mehta¹  Ritu Rawat¹  Vikram K. Mahajan¹  Saurabh Sharma²  Pushpinder S. Chauhan¹  Mrinal Gupta¹ 

[1] Department of Dermatology, Venereology & Leprosy, Dr. Rajendra Prasad Government Medical College, Kangra (Tanda), Himachal Pradesh — 176001, India;;Department of Pathology, Dr. Rajendra Prasad Government Medical College, Kangra (Tanda), Himachal Pradesh — 176001, India.

关键词: eosinophilia;    erythroderma;    hypereosinophilic syndrome;    itch;    hydroxycarbamide;    palmoplantar hyperkeratosis;    pruritus;    Sézary syndrome;   

DOI  :  10.3315/jdcr.2014.1185

学科分类：皮肤病学

来源: Specjalisci Dermatolodz

【 摘 要 】

Idiopathic hypereosinophilic syndrome (HES) is a rare and potentially lethal disorder characterized by persistently elevated eosinophil counts without any underlying causes. Two variants, the myeloproliferative and lymphocytic hypereosinophilic syndrome, have been identified. The symptoms are variable and related to the organs involved (cardiovascular system, skin, central and peripheral nervous system, gastrointestinal tract, eyes). Skin lesions can be the dominating and/or presenting symptom in about 50% of patients.

【 授权许可】

Unknown