Two Egyptian cases of lipoid proteinosis successfully treated with acitretin

Journal of Dermatological Case Reports

Ola Ahmed Bakry²  Mohamed Ahmed Basha¹  Nanees Shawky Houla² 

[1] Department of Dermatology, Andrology and S.T.Ds, Faculty of Medicine, Menoufiya University, Shebin El Kom, Menoufiya, Egypt;;Department of Pathology, Faculty of Medicine, Menoufiya University, Shebin El Kom, Menoufiya, Egypt.

关键词: acitretin;    blister;    genodermatoses;    hoarseness;    lipoid proteinosis;    pharynx;    throat;   

DOI  :  10.3315/jdcr.2014.1168

学科分类：皮肤病学

来源: Specjalisci Dermatolodz

【 摘 要 】

Lipoid proteinosis (Urbach-Wiethe disease) is a rare progressive autosomal recessive disorder, characterized histologically by deposition of periodic acid Schiff-positive, diastase resistant, hyaline-like material into the skin, upper aerodigestive tract, and internal organs.

【 授权许可】

Unknown