Caudal duplication syndrome: imaging evaluation of a rare entity in an adult patient

Developmental Biology

Tianshen Hu¹  Kristen Bishop¹  Travis Browning¹ 

[1] Department of Radiology, University of Texas Southwestern Medical Center, 5323 Harry Hines Blvd, Dallas, TX 75390-8896, USA$$

关键词: Intraductal papillary mucinous neoplasia;    Pancreas;    Magnetic resonance;    Ultrasonography;    Cystic;   

DOI  :  10.1016/j.radcr.2015.12.001

学科分类：医学（综合）

来源: University of Washington * Department of Radiology

【 摘 要 】

Several theories have been put forth to explain the complex yet symmetrical malformations and the myriad of clinical presentations of caudal duplication syndrome. Hereby, reported case is a 28-year-old female, gravida 2 para 2, with congenital caudal malformation who has undergone partial reconstructive surgeries in infancy to connect her 2 colons. She presented with recurrent left lower abdominal pain associated with nausea, vomiting, and subsequent feculent anal discharge. Imaging reveals duplication of the urinary bladder, urethra, and colon with with cloacal malformations and fistulae from the left-sided cloaca, uterus didelphys with separate cervices and vaginal canals, right-sided aortic arch and descending thoracic aorta, and dysraphic midline sacrococcygeal defect. Hydronephrosis of the left kidney with left hydroureter and inflammation of one of the colons were suspected to be the cause of the patient’s acute complaints. She improved symptomatically over the course of her hospitalization stay with conservative treatments. The management for this syndrome is individualized and may include surgical intervention to fuse or excise the duplicated organs.

【 授权许可】

Unknown