Isolated non-compaction of the left ventricle

South African Journal of Child Health

Vinayak Yadavrao Kshirsagar¹  Shriganesh Vasudev Patil¹  Minhajuddin Ahmed¹  Sylvia Michael Colaco¹ 

[1]Krishna Institute of Medical Sciences, Deemed University, Karad, India

关键词: Non-compaction;    newborn;    left ventricle;    cardiac failure;   

DOI  :  

学科分类：农业科学（综合）

来源: Health and Medical Publishing Group

【 摘 要 】

Isolated left ventricular non-compaction (LVNC) is a rare congenital disorder caused by failure of normal embryogenesis of the endocardium and myocardium in utero, resulting in prominent ventricular trabeculations with deep intertrabecular recesses. Patients may be asymptomatic or may present with refractory cardiac failure. The best modality of diagnosis is based on echocardiographic diagnostic criteria. Prognosis remains poor for patients with impaired systolic left ventricular function, as treatment options are very limited. We report the case of 2-month-old infant presenting with congestive cardiac failure diagnosed as isolated LVNC on echocardiography.

【 授权许可】

Unknown