Revista da Sociedade Brasileira de Fonoaudiologia | |
Audiologic findings in individuals with Steinert's myotonic dystrophy | |
Lucena, Rita1  Argolo, Lorena Silva de1  União Metropolitana de Educação e Cultura, Lauro de Freitas, Brasil1  Guimarães, Camila Vila-Nova de Freitas1  Universidade Federal da Bahia, Salvador, Brasil1  Lins, Lorene Lemos1  Universidade do Estado da Bahia, Salvador, Brasil1  Padovani, Carla Marcondes César Affonso1  Fernandes, Luciene Cruz1  Queirós, Fernanda Costa de1  Hospital Santo Antonio, Salvador, Brasil1  | |
关键词: Myotonic dystrophy/physiopathology; Myotonic dystrophy/complications; Hearing disorders; Hearing; Acoustic impedance tests; Stapedius; Eustachian tube; Reflex/genetics; | |
DOI : 10.1590/S1516-80342008000400008 | |
来源: Sociedade Brasileira de Fonoaudiologia | |
【 摘 要 】
PURPOSE: To identify the main hearing disorders in individuals with Steinert's myotonic dystrophy.METHODS: Five individuals were submitted to tonal and vocal audiometry, acoustic impedance tests, examination of Eustaquian tube function, acoustic reflex investigation, and acoustic reflex decay. They also answered two questionnaires: a) Performance of auditory function; b) Psycho-acoustic-social investigation.RESULTS: The study showed that 60% of the sample presented normal hearing thresholds, 10% had conductive hearing loss and 30% had hearing loss in high frequencies. Concerning acoustic reflexes, it was observed that 30% of the subjects presented deficits at 0.5 and 1 kHz and 40% at 2 and 4 kHz. Acoustic reflex decay was observed in 10% of the sample at 0,5 and 1 kHz.CONCLUSION: The study showed that the typical auditory profile of high-frequencies hearing loss was observed in 30% of the sample.
【 授权许可】
Unknown
【 预 览 】
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RO201912010141852ZK.pdf | 247KB | download |