Blaschko-linear “Congenital Mixed Hemato-lymphangio-keratoma Serpiginosum” Naeviforme: A New Hybrid Entity or Various Morphological Reflections of the Two Different Vascular Abnormalities?

The Journal of Clinical and Aesthetic Dermatology

Serdar Altinay¹  Betul Tas²  Aysel Çağlar³ 

[1] Dr. Altinay is with the Health Sciences University, Bakirkoy Sadi Konuk Research and Training Hospital, Department of Pathology, in Istanbul, Turkey.;Dr. Tas is with the Health Sciences University, Istanbul Bagcilar Research and Training Hospital, Department of Dermatology in Istanbul, Turkey.;Dr. alar is with the Health Sciences University, Istanbul Bagcilar Research and Training Hospital, Department of Pathology in Istanbul, Turkey.

关键词: Lymphangioma;    hemangioma;    lymphangiokeratoma;    verrucous hemangioma;    angiokeratoma circumscriptum;    angioma serpiginosum;   

DOI  :  

学科分类：医学（综合）

来源: Matrix Medical Communications, LLC

【 摘 要 】

We present the case of a 15-year-old girl who presented with an unusual grouping of lesions on her upper left leg. The lesions had been present since birth. The patient had five different types of lesions: 1) transparent grouped or scattered yellowish vesicles; 2) keratotic-surfaced, grouped dark-yellowish papules; 3) bright-red grouped papules; 4) keratotic-surfaced grouped dark-red papules; and 5) patchy, punctate, and erythematous red macules. All of the lesions were intertwined along the lines of Blaschko and were in the form of irregular serpiginous plaques. Histopathological examinations of the lesions showed three main histological features, and diagnoses of the lesions were made as lymphangioma circumscriptum, lymphangiokeratoma, and verrucous hemangioma. To the best of our knowledge, such intertwined lesions have never been reported in the literature. Hence, we suggest that the name of this unique combination of lesions be “congenital nevoid mixed hemato-lymphangio-keratoma serpiginosum."

【 授权许可】

Unknown