Biliary mucinous cystic neoplasm mimicking a hydatid cyst: a case report and literature review

BMC Gastroenterology

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[1] 0000 0000 9401 2774, grid.414980.0, Department of Pathology, Jewish General Hospital, Montreal, QC, Canada;0000 0000 9401 2774, grid.414980.0, Division of General Surgery, Jewish General Hospital, 3755 Côte-Sainte-Catherine, H3T 1E2, Montréal, QC, Canada;0000 0000 9401 2774, grid.414980.0, Division of General Surgery, Jewish General Hospital, 3755 Côte-Sainte-Catherine, H3T 1E2, Montréal, QC, Canada;0000 0000 9064 4811, grid.63984.30, Division of Urology, McGill University Health Center, Montréal, QC, Canada;

关键词: Biliary cystadenoma;    Biliary mucinous cystic neoplasm;    Hydatid disease;    Investigation;    Management;   

DOI  :  10.1186/s12876-019-1001-5

来源: publisher

【 摘 要 】

BackgroundBiliary mucinous cystic neoplasms are rare cystic lesions of the liver which carry pre-malignant potential. Given the scarcity of reports in the literature, they pose a considerable challenge to clinical management, particularly with regards to accurate pre-operative diagnosis.Case presentationWe present the case of a 37-year-old Tunisian woman who presented with subacute right upper quadrant pain and a large multi-loculated cystic lesion, most consistent with a hydatid cyst. She underwent an open right hepatectomy, and pathology surprisingly revealed a biliary mucinous cystadenoma. Herein, we review the current literature on biliary mucinous cystic neoplasms, with a particular emphasis on diagnostic investigations, key radiological features and optimal treatment modalities.ConclusionBiliary mucinous cystic neoplasms require a high index of suspicion and should be managed with complete surgical resection, as conservative techniques are associated with high recurrence rates. Considering the potential for malignant transformation, periodical surveillance imaging is recommended in the post-operative period.

【 授权许可】

CC BY