Oftal mokhirurgiya | |
Хирургическое лечение врожденной глаукомы при синдроме Франк-Каменецкого (клинический случай) | |
А. В. Сидорова1  А. М. Демчинский1  К. Г. Хлиян1  А. В. Оплетина1  | |
[1] ФГАУ «МНТК «Микрохир ургия г лаза» им. акад. С.Н. Федорова» Минздрава России», Москва | |
关键词: mesenchymal; dystrophy; syndrome; Frank-Kamenetsky; glaucoma; surgery; non-penetrating deep sclerectomy; мезенхимальная; дистрофия; синдром; Франк-Каменецкий; глаукома; непроникающая глубокая склерэктомия.; | |
DOI : 10.25276/0235-4160-2015-3-19-22 | |
学科分类:眼科学 | |
来源: M H T K Mikrokhirurgiya Glaza | |
【 摘 要 】
Purpose . To submit clinical features and the effectiveness of surgical treatment of patients with glaucoma associated with the Frank-Kamenetsky’s syndrome. Material and method.We examined two patients with the Frank-Kamenetsky’s syndrome. Microinvasive non-penetrating deep sclerectomy was performed in both eyes of these patients. Results.The examination of patients detected the following features: x-linked recessive type of inheritance, decreased keratometry parameters with an axial length increase of the eye, specific changes in the anterior segment of the eye: posterior embryotoxon, bluish sclera, unusual iris structure, specific goniodisgenesis and glaucoma starting in adolescence. The combination of these features allowed us to diagnose the Frank-Kamenetsky’s syndrome. The operation and postoperative period were uncompli cated. The intraocular pressure was compensated during the entire follow-up periods. Conclusion.The described clinical cases demonstrate the clinical features of the Frank-Kamenetsky’s syndrome with a specific genetic link. A tolerance to the medical treatment with a fast progression is typical for this type of glaucoma. Surgical treatment allows to compensate the stable hydrodynamic indices of intraocular pressure, to preserve and improve visual function in these patients.
【 授权许可】
CC BY
【 预 览 】
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RO201904035240158ZK.pdf | 185KB | download |