Хирургическое лечение врожденной глаукомы при синдроме Франк-Каменецкого (клинический случай)

Oftal mokhirurgiya

А. В. Сидорова¹  А. М. Демчинский¹  К. Г. Хлиян¹  А. В. Оплетина¹ 

[1] ФГАУ «МНТК «Микрохир ургия г лаза» им. акад. С.Н. Федорова» Минздрава России», Москва

关键词: mesenchymal;    dystrophy;    syndrome;    Frank-Kamenetsky;    glaucoma;    surgery;    non-penetrating deep sclerectomy;    мезенхимальная;    дистрофия;    синдром;    Франк-Каменецкий;    глаукома;    непроникающая глубокая склерэктомия.;   

DOI  :  10.25276/0235-4160-2015-3-19-22

学科分类：眼科学

来源: M H T K Mikrokhirurgiya Glaza

【 摘 要 】

Purpose . To submit clinical features and the effectiveness of surgical treatment of patients with glaucoma associated with the Frank-Kamenetsky’s syndrome. Material and method.We examined two patients with the Frank-Kamenetsky’s syndrome. Microinvasive non-penetrating deep sclerectomy was performed in both eyes of these patients. Results.The examination of patients detected the following features: x-linked recessive type of inheritance, decreased keratometry parameters with an axial length increase of the eye, specific changes in the anterior segment of the eye: posterior embryotoxon, bluish sclera, unusual iris structure, specific goniodisgenesis and glaucoma starting in adolescence. The combination of these features allowed us to diagnose the Frank-Kamenetsky’s syndrome. The operation and postoperative period were uncompli cated. The intraocular pressure was compensated during the entire follow-up periods. Conclusion.The described clinical cases demonstrate the clinical features of the Frank-Kamenetsky’s syndrome with a specific genetic link. A tolerance to the medical treatment with a fast progression is typical for this type of glaucoma. Surgical treatment allows to compensate the stable hydrodynamic indices of intraocular pressure, to preserve and improve visual function in these patients.

【 授权许可】

CC BY