期刊论文详细信息
Pulmonary Circulation | |
Late-onset pulmonary arterial hypertension in repaired D-transposition of great arteries: an uncommon complication: | |
JananiBaskaran1  | |
关键词: Mustard; congenital; cyanotic; right ventricle; baffle; | |
DOI : 10.1177/2045893217699228 | |
学科分类:医学(综合) | |
来源: Sage Journals | |
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【 摘 要 】
Late-onset pulmonary arterial hypertension (PAH) is a rare but fatal complication in patients with childhood surgical repair of dextro-transposition of great arteries (D-TGA), especially with the Mustard and Senning procedures. The pathogenic mechanisms of PAH in patients with repaired D-TGA are not well understood and treatment is not standardized. In this manuscript, we present a case of late-onset PAH in an adult D-TGA patient after Mustard repair and discuss the pathogenic mechanisms, diagnosis, and treatment of pulmonary hypertension in repaired D-TGA.【 授权许可】
CC BY
【 预 览 】
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RO201904022369361ZK.pdf | 157KB | ![]() |