Rare Coexistence of Major Lung Pathologies

Advances in Pulmonary Hypertension

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关键词: Cardiology;    Pulmonology;    Rheumatology;    Pediatrics;    Psychosocial Issues;    WHO Group 1- Pulmonary Arterial Hypertension;    WHO Group 5- Pulmonary hypertension with unclear multifactorial mechanisms;    PH Medications;    Echocardiography;    CT Scans;    Electrocardiogram;    Pulmonary Function Tests;    Arterial blood gas;    Surgical Interventions;    Anatomy;    Physiology/Pathophysiology;    symptoms;    Gender;    PH;    Research;    Managing PH Emergencies;    Neonatal;    early childhood;    Social Security Disability;    Support;    Drug;    Toxin-induced;    Associated Diseases;    HIV Infection;    Mixed restrictive;    obstructive pattern;    bronchiolitis obliterans;    hematologic disorder;    Oral therapy;    IV therapy;    Subcutaneous therapy;    Inhaled therapy;    Calcium channel blockers;    Phosphodiesterase Inhibitors (PDE-5 Inhibitors);    Prostacyclin;    Endothelin Receptor Antagonists;    nitric oxide;    Vasodilator study;    Acute vasodialtor challenge;    6-Minute Walk Test;    Spirometry;    Lung Volumes;    FVC/Clco>;    1.6;    endothelial dysfunction;    syncope;    tachycardia;    dyspnea;    hypoxia;    chest pain;    Angiogram;    Epidemiology;   

DOI  :  

学科分类：医学（综合）

来源: Pulmonary Hypertension Association

【 摘 要 】

Presentation: A 40-year-old African American female with past history of congenital heart murmurs of unknown etiology, iron deficiency anemia, and intellectual disability secondary to newborn shaken baby syndrome presented to the emergency department with worsening dyspnea, cough, sore throat, and fatigue. Family history was significant for Wegener’s granulomatosis and lung cancer. Social history was negative for tobacco, alcohol, or illicit drug use. She lives at home with her sister as her legal caregiver. Workup revealed tachycardia, III/VI holosystolic murmur, right axis deviation on electrocardiogram (EKG), and respiratory alkalosis on arterial blood gas (ABG). She was found to have bilateral upper lobe infiltrates and hilar lymphadenopathy as well as an enlarged pulmonary artery on computed tomography (CT) scan. She was admitted and treated empirically for pneumonia with antibiotics without clinical improvement. She was then referred to the pulmonary clinic for further clinical workup and evaluation of radiographic changes.

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