Pulmonary Arterial Hypertension Combined with a High Cardiac Output State: Three Remarkable Cases:

Pulmonary Circulation

Onno A.Spruijt¹ 

关键词: abernethy malformation;    congenital extrahepatic portosystemic venous shunt;    congenital extrahepatic portosystemic shunt;    pulmonary arterial hypertension;   

DOI  :  10.4103/2045-8932.113185

学科分类：医学（综合）

来源: Sage Journals

【 摘 要 】

A congenital extrahepatic portosystemic venous shunt (CEPVS), also known as an Abernethy malformation, is a rare cause of pulmonary arterial hypertension (PAH). In this case series, we describe three male patients of 30, 23, and 27 years of age with PAH due to a CEPVS. In all three patients, a right heart catheterization revealed a high cardiac output. The aim of this case series is to make pulmonary hypertension physicians aware of the possibility of a CEPVS when PAH is accompanied with a high cardiac output state.

【 授权许可】

CC BY