PEComa of the uterus with coexistence of situs inversus totalis, a case report and literature review

Diagnostic Pathology

En-hua Wang³  Xiao-Yan Pang¹  Yi Zhao¹  Qing-chang Li³  Xue-shan Qiu³  Ting-ting Liu²  Yang Han³ 

[1] Department of Obstetrics and Gynecology, The First Affiliated Hospital of China Medical University, Shenyang, China;Department of General Surgery, The First Affiliated Hospital of China Medical University, Shenyang, China;Department of Pathology, The First Affiliated Hospital of China Medical University, Shenyang, China

关键词: Situs inversus totalis;    Uterus;    PEComa;   

Others  :  1225911
DOI  :  10.1186/s13000-015-0351-8

 received in 2015-05-14, accepted in 2015-07-09,  发布年份 2015

【 摘 要 】

PEComas are a group of very rare mesenchymal neoplasms, which express myogenic and melanocytic markers, such as HMB-45 and actin. Situs inversus totalis represents a complete left to right side transposition of the asymmetrical thoracic and abdominal organs and incorporates dextrocardia. The presence of uterus PEComa in the setting of situs inversus totalis is extremely rare. Here, we report a case of PEComa of uterus with coexistence of situs inversus totalis and review the literatures. To the best of our knowledge this is the fist report of a uterus PEComa patient with situs inversus totalis.

【 授权许可】

   
2015 Han et al.

【 图 表 】

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