Synchronous plexiform neurofibroma in the arytenoids and neurofibroma in the parapharynx in a patient with non-neurofibromatosis: a case report

Journal of Medical Case Reports

Seung Hoon Woo³  Jin Pyeong Kim²  Hyun Seok Shim²  Hee Young Son¹ 

[1] Department of Otolaryngology, Thyroid/Head and Neck Cancer Center of The Dongnam Institute of Radiological & Medical Sciences (DIRAMS), Pusan, Korea;Department of Otolaryngology, Gyeongsang National University, Jinju, Korea;Institute of Health Sciences, Gyeongsang National University, Jinju, Korea

关键词: Plexiform neurofibroma;    Laryngeal tumor;    Laryngeal neurofibroma;   

Others  :  1195138
DOI  :  10.1186/1752-1947-7-15

 received in 2012-09-21, accepted in 2012-11-28,  发布年份 2013

【 摘 要 】

Introduction

Plexiform neurofibroma of the larynx is a rare disease. In this report, we present a plexiform neurofibroma in the arytenoids and neurofibroma in the parapharynx detected coincidently.

Case presentation

A 56-year-old Asian woman presented with respiratory distress and episodes of apnea at night. A solitary mass from the left arytenoids was found to be nearly obstructing the airway and causing the sleep apnea. There was also a parapharynx mass protruding into the pharynx. The parapharynx tumor was removed with the lateral incision approach, and the arytenoid tumor was removed with a transoral carbon dioxide laser. The pathologic diagnosis was plexiform neurofibroma for the arytenoid mass and neurofibroma for the parapharynx mass.

Conclusion

We have reported an extremely rare case of plexiform neurofibroma in the arytenoids and neurofibroma in the parapharynx. This entity may be considered in the differential diagnosis of all laryngeal and parapharynx masses.

【 授权许可】

   
2013 Son et al.; licensee BioMed Central Ltd.

【 图 表 】

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