Hypothesis on etiopathogenesis, congenital or acquired, of an imperforate distal ureter: a case report

Journal of Medical Case Reports

P. Caione²  T. Luca³  G. Privitera³  S. Gerocarni Nappo²  S. Castorina¹  Vincenzo Bagnara³ 

[1]Department of Biomedical and Biotechnological Sciences, University of Catania, Catania, 95125, Italy

[2]Division of Urology-Andrology, Department of Paediatric Nephrology-Urology, “Bambino Gesu” Children’s Hospital, Research Institute, Rome, Italy

[3]“G.B. Morgagni” Mediterranean Foundation, Catania, 95125, Italy

关键词: Ureteropelvic junction obstruction;    Ureteral atresia;    Pyeloplasty;    Imperforate distal ureter;   

Others  :  1233275
DOI  :  10.1186/s13256-015-0711-8

 received in 2015-02-28, accepted in 2015-09-15,  发布年份 2015

【 摘 要 】

Introduction

Ureteral atresia is a rare disease usually associated with a non-functioning kidney. Its association with other urinary anomalies is rare.

Case presentation

In this study we discuss the possibility of congenital or acquired etiology of a right imperforate distal ureter. Here we report the case of 11-month-old white boy with a right ureteropelvic junction obstruction. He underwent a right pyeloplasty when he was 11-months old, and 3 weeks after surgery a cystoscopy was performed. Two months after the first operation, he underwent a right ureteral meatoplasty and a new pyeloplasty.

Conclusions

To the best of our knowledge, few cases of imperforate distal ureter have been described in the literature. The suspicion of a non-patent terminal ureter, occurring during upper urinary tract surgery, must be intraoperatively clarified to preserve the renal function and to avoid more complex surgical approaches.

【 授权许可】

   
2015 Bagnara et al.

【 图 表 】

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